Feocromocitoma y paraganglioma
- C. Guillín 1
- I. Bernabeu 1
- I.A. Rodríguez-Gómez 2
- F.F. Casanueva 2
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1
Complexo Hospitalario Universitario de Santiago
info
Complexo Hospitalario Universitario de Santiago
Santiago de Compostela, España
- 2 Unidad de Endocrinología y Nutrición. Hospital HM Modelo. La Coruña. España
ISSN: 0304-5412
Datum der Publikation: 2016
Titel der Ausgabe: Enfermedades endocrinológicas y metabólicas (II) Patología suprarrenal
Serie: 12
Nummer: 14
Seiten: 795-801
Art: Artikel
Andere Publikationen in: Medicine: Programa de Formación Médica Continuada Acreditado
Zusammenfassung
Introduction Chromaffin tumors of the adrenal medulla and the sympathetic ganglia are known as pheochromocytoma and paraganglioma, respectively. They are rare diseases, in most cases histologically benign, but potentially lethal due to the overproduction of catecholamines. History and clinical examination Clinical presentation depends on the activation of adrenergic receptors. Usually patients have labile and refractory hypertension, and other signs and symptoms, which include the classic triad (headache, sweating and tachycardia), adrenal paroxysms, hypertensive retinopathy, cardiomyopathy or anorexia, among others. Evaluation After establishing the biochemical confirmation of catecholamine excess, imaging techniques of choice to locate the tumor are the computed tomography and the magnetic resonance. Treatment Treatment of choice is the complete resection of the tumor, only after a correct alpha and beta adrenergic blockade, in order to control blood pressure and prevent intraoperative paroxysms.
Bibliographische Referenzen
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